Biotin Metabolism{}Phosphoenolpyruvate carboxykinase deficiency 1 (PEPCK1){}Fructose-1,6-diphosphatase deficiency{}Glycogen Storage Disease Type 1A (GSD1A) or Von Gierke Disease{}2-Hydroxyglutric Aciduria (D And L Form){}Threonine and 2-Oxobutanoate Degradation{}2-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency{}2-ketoglutarate dehydrogenase complex deficiency{}3-Methylglutaconic Aciduria Type IV{}3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency{}3-Methylcrotonyl Coa Carboxylase Deficiency Type I{}3-Methylglutaconic Aciduria Type I{}3-Methylglutaconic Aciduria Type III{}3-hydroxyisobutyric acid dehydrogenase deficiency{}3-hydroxyisobutyric aciduria{}4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency{}Transfer of Acetyl Groups into Mitochondria{}Citric Acid Cycle{}Fatty Acid Biosynthesis{}Lactic Acidemia{}Propionic Acidemia{}Isovaleric acidemia{}Congenital lactic acidosis{}Methylmalonic Aciduria Due to Cobalamin-Related Disorders{}Malonic Aciduria{}Isovaleric Aciduria{}Methylmalonic Aciduria{}Alanine Metabolism{}Ammonia Recycling{}Beta-Ketothiolase Deficiency{}Biotinidase Deficiency{}Pyruvate Carboxylase Deficiency{}Multiple carboxylase deficiency, neonatal or early onset form{}Isobutyryl-coa dehydrogenase deficiency{}Malonyl-coa decarboxylase deficiency{}Pyruvate Dehydrogenase Complex Deficiency{}Mitochondrial complex II deficiency{}Pyruvate Decarboxylase E1 Component Deficiency (PDHE1 Deficiency){}Methylmalonate Semialdehyde Dehydrogenase Deficiency{}Fumarase deficiency{}Pyruvate dehydrogenase deficiency (E3){}Pyruvate dehydrogenase deficiency (E2){}Pyruvate kinase deficiency{}Succinic semialdehyde dehydrogenase deficiency{}Valine, Leucine and Isoleucine Degradation{}Maple Syrup Urine Disease{}Glycogenosis, Type IA. Von gierke disease{}Gluconeogenesis{}Glutamate Metabolism{}Glycogenosis, Type IB{}Glycogenosis, Type IC{}Homocarnosinosis{}Hyperinsulinism-Hyperammonemia Syndrome{}Primary Hyperoxaluria Type I{}Primary hyperoxaluria II, PH2{}Triosephosphate isomerase{}Leigh Syndrome{}Pyruvate Metabolism{}Propanoate Metabolism